Viola R W, Kahn A, Pottenger L A
Section of Orthopaedic Surgery, University of Chicago, Illinois 60637.
J Pediatr Orthop. 1991 Sep-Oct;11(5):671-5.
We report the orthopaedic management of a child with macrodystrophia lipomatosa of the medial aspect of the right lower limb. Bony and soft tissue overgrowth of the medial aspect of the lower limb resulted in valgus deformities at the subtalar joint, ankle, knee, and hip. The paraxial distribution, which has not been previously reported, suggests that the condition may be caused by alteration of somatic cells during limb bud development.
我们报告了一名右下肢内侧患有巨脂性营养障碍的儿童的骨科治疗情况。下肢内侧的骨骼和软组织过度生长导致距下关节、踝关节、膝关节和髋关节出现外翻畸形。这种尚未见先前报道的近轴分布表明，该病可能是由肢体芽发育过程中体细胞的改变引起的。
