Loro A, Francechi F, Dal Lago A
Paediatrics Department, Dodoma Regional Hospital, Tanzania.
Ethiop Med J. 1995 Jul;33(3):187-92.
Macrodystrophia lipomatosa, a rare form of localized gigantism of unknown cause, is characterized by a dramatic overgrowth of all the mesenchymal elements, particularly the fibroadipose tissue, of one or more digits of the foot or hand. Of the known forms, static and progressive (1), we report the case of an African patient, of Bantu origin, who had a progressive deformity of his left hand.
巨脂性营养障碍,一种病因不明的罕见局限性巨大症,其特征是足部或手部一个或多个手指的所有间充质成分,特别是纤维脂肪组织显著过度生长。在已知类型中,有静止型和进行型(1),我们报告一例来自班图族的非洲患者,其左手出现进行性畸形。