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遗传性出血性毛细血管扩张症合并肺动静脉畸形并表现为血胸。

Hereditary hemorrhagic telangiectasia associated with pulmonary arteriovenous malformations presenting as hemothorax.

作者信息

Elmali Muzaffer, Akan Huseyin, Findik Serhat, Kale Melike, Celenk Cetin

机构信息

Department of Radiology, Faculty of Medicine, Ondokuz Mayis University Samsun, Turkey.

出版信息

J Thorac Imaging. 2008 Nov;23(4):295-7. doi: 10.1097/RTI.0b013e3181820867.

Abstract

A 51-year-old woman was admitted to emergency unit complaining of sudden onset chest pain. The patient had a family history of hereditary hemorrhagic telangiectasia. Thorax computed tomographic angiography demonstrated high-density left pleural effusion, and 3 giant arteriovenous malformations. Thoracentesis revealed hemorrhagic fluid. We present successful coil embolization of pulmonary arteriovenous malformations associated with hereditary hemorrhagic telangiectasia.

摘要

一名51岁女性因突发胸痛被送入急诊科。该患者有遗传性出血性毛细血管扩张症家族史。胸部计算机断层血管造影显示左侧胸腔积液密度增高,并有3处巨大动静脉畸形。胸腔穿刺抽出了血性液体。我们报告了对与遗传性出血性毛细血管扩张症相关的肺动静脉畸形成功进行弹簧圈栓塞治疗的病例。

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