Yale University School of Medicine, New Haven, CT 06520-8042, USA.
Chest. 2010 Mar;137(3):705-7. doi: 10.1378/chest.09-0344.
Spontaneous hemothorax as a result of a ruptured pulmonary arteriovenous malformation (PAVM) is a life-threatening event and requires immediate interventional therapy. We present two patients who survived following emergent embolization. Definitive thoracentesis was delayed until embolization was performed. The tamponade provided by the hemothorax may have prevented exsanguination, suggesting to us that drainage of blood from the pleural space should be delayed until the PAVM has been treated. Hemorrhage from a PAVM may be the first manifestation of hereditary hemorrhagic telangiectasia. Genetic testing and screening for other family members should be considered.
自发性血胸是由于肺动静脉畸形破裂引起的，是一种危及生命的事件，需要立即进行介入治疗。我们介绍了两位接受紧急栓塞治疗后幸存的患者。在进行栓塞治疗之前，明确的胸腔穿刺被延迟了。血胸引起的填塞可能防止了失血，这提示我们，应该延迟从胸腔引流血液，直到 PAVM 得到治疗。PAVM 的出血可能是遗传性出血性毛细血管扩张症的首发表现。应考虑进行基因检测和对其他家庭成员进行筛查。
