Weinman D, Stewart M I, Woodley D T, Garcia G
Department of Medicine, Stanford University Medical Center, California.
Am J Gastroenterol. 1991 Oct;86(10):1518-22.
Epidermolysis bullosa acquisita (EBA) is a well-defined, blistering disorder of the skin associated with autoantibodies to type VII collagen. Although esophageal pathology is common in children with hereditary dystrophic forms of epidermolysis bullosa, esophageal problems have not been reported previously in patients with bona fide EBA. In this report, a 71-yr-old white female with longstanding EBA presented with recurrent dysphagia and multiple esophageal webs that responded to esophageal dilatation.
获得性大疱性表皮松解症(EBA)是一种明确的皮肤水疱性疾病,与抗VII型胶原蛋白自身抗体相关。虽然食管病变在遗传性营养不良型大疱性表皮松解症患儿中很常见,但此前尚未有关于真正的EBA患者食管问题的报道。在本报告中,一名患有长期EBA的71岁白人女性出现反复吞咽困难和多个食管蹼,经食管扩张治疗后症状缓解。