Schattenkirchner S, Lémann M, Prost C, Caux F, Guigui B, Cadot M, Bertheau P, Grateau C, Heller M
Centre d'Etudes et de Diagnostic des Maladies Bulleuses, Hôpital Saint-Louis, Paris, France.
Am J Gastroenterol. 1996 Aug;91(8):1657-9.
Epidermolysis bullosa acquisita is a rare autoimmune subepidermal bullous disease that affects both the skin and mucosae and is frequently associated with Crohn's disease. We report the case of a 27-yr-old man with Crohn's disease who presented with localized epidermolysis bullosa acquisita of the esophagus, without any other mucosal or cutaneous lesions. The patient was successfully treated with sulfasalazine.
获得性大疱性表皮松解症是一种罕见的自身免疫性表皮下大疱性疾病,可累及皮肤和黏膜,常与克罗恩病相关。我们报告一例27岁克罗恩病男性患者,其表现为局限性食管获得性大疱性表皮松解症,无任何其他黏膜或皮肤损害。该患者用柳氮磺胺吡啶治疗成功。