Gavaskar K G Ashok Sunil, Chowdary Naveen
Mahatma Gandhi Medical College and Research Institute, Pondy-Cuddalore Main Road, Pillayarkuppam, Pondicherry, 607 402, India,
J Child Orthop. 2009 Apr;3(2):109-14. doi: 10.1007/s11832-009-0163-z. Epub 2009 Feb 20.
Windblown hand is a congenital anomaly characterized by multiple hand deformities. The condition is extremely rare as shown by the paucity of cases reported in the literature. The deformities, which can result in a cosmetically unsatisfactory appearance and, if left untreated, maladaptive behavior, are progressive in nature. Consequently early treatment is necessary.
We operated upon 23 hands in 18 patients (age range at surgery 6 months to 16 years) at a tertiary care center over a period of 7 years. The patients were followed for an average period of 7 years. The surgical approach was chosen based on the severity of the condition according to Zancolli and Zancolli's classification [Hand Clin 1:443-456 (1985)].
According to the criteria of Wood and Biondi [J Hand Surg 15A:431-438 (1990)], of the 23 hands operated upon, 17 had excellent cosmetic results, and 15 had excellent functional results. The results were better in patients undergoing early surgery-before the age of 2 years. Relapse of the deformity to a lesser extent than the original condition was seen in two hands at the last follow up.
Definitive conclusions on this condition cannot be drawn due to limited experience in the surgical management of this rare condition. We believe that early surgical management is probably the best option available for the patient based on the results obtained. Early surgery and good post-operative compliance from patients can facilitate successful management of this rare condition with predictable results.
风铲手是一种以多种手部畸形为特征的先天性异常。如文献报道的病例稀少所示,这种情况极为罕见。这些畸形会导致外观上不尽人意,若不治疗,还会引发适应不良行为,且本质上是进行性的。因此,早期治疗很有必要。
在7年时间里,我们在一家三级医疗中心对18例患者(手术年龄范围为6个月至16岁)的23只手进行了手术。对患者进行了平均7年的随访。根据赞科利和赞科利的分类法[《手外科临床》1:443 - 456(1985)],依据病情严重程度选择手术方式。
根据伍德和比昂迪的标准[《手外科杂志》15A:431 - 438(1990)],在接受手术的23只手中,17只获得了极佳的美容效果,15只获得了极佳的功能效果。在2岁之前接受早期手术的患者效果更好。在最后一次随访时,有两只手出现了畸形复发,程度比原来轻。
由于在这种罕见疾病的手术治疗方面经验有限,无法得出关于这种疾病的确切结论。基于所获得的结果,我们认为早期手术治疗可能是患者的最佳选择。早期手术以及患者良好的术后依从性有助于成功治疗这种罕见疾病并获得可预测的结果。