Zemlyak Alla, Hwang Sonya, Chalas Eva, Pameijer Colette R J
Stony Brook University Medical Center, Stony Brook, NY, USA.
J Gastrointest Cancer. 2008;39(1-4):104-6. doi: 10.1007/s12029-009-9064-0. Epub 2009 Mar 31.
Extrauterine endometrial stromal sarcoma (ESS) is a rare neoplasm. Little is known about its pathophysiology or best treatment approach.
We are describing a case of extrauterine ESS in a 70-year-old woman on hormone replacement therapy and with a history of endometriosis. We also present a brief review of the literature on ESS and its relationship to endometriosis and hormonal therapy.
Complete resection should remain the treatment of choice for ESS. Unresectable or metastatic low-grade ESS may respond well to progestin therapy, but outcomes of high-grade ESS tend to be poor.
子宫外子宫内膜间质肉瘤（ESS）是一种罕见的肿瘤。对其病理生理学或最佳治疗方法知之甚少。
我们正在描述一名70岁接受激素替代治疗且有子宫内膜异位症病史的女性发生子宫外ESS的病例。我们还简要回顾了关于ESS及其与子宫内膜异位症和激素治疗关系的文献。
完整切除仍应是ESS的首选治疗方法。不可切除或转移性低级别ESS可能对孕激素治疗反应良好，但高级别ESS的预后往往较差。
