Ranjan Rakesh, Tewari Rajiv, Kumar Sushil
Department of Neurosurgery, St. Stephen's Hospital, Delhi, India.
Childs Nerv Syst. 2009 Sep;25(9):1121-4. doi: 10.1007/s00381-009-0870-2. Epub 2009 Apr 1.
Spinal intradural extramedullary ependymal cyst is a very rare entity with only few cases reported in the literature. Its association with congenital dermal sinus has not been described so far. We present a unique report of a 3-year-old male child who presented with spastic quadriparesis with a trophic ulcer in the right great toe of 1-year duration. He harbored a congenital dermal sinus in the cervical spine since birth. Intraoperatively, the sinus was associated with an intradural cyst which proved to be an ependymal cyst on histopathological examination. The clinical profile along with review of literature of this rare entity is presented.
脊髓硬膜内髓外室管膜囊肿是一种非常罕见的疾病,文献中仅报道了少数病例。迄今为止,尚未描述其与先天性皮样窦的关联。我们报告了一例独特的病例,一名3岁男童,表现为痉挛性四肢瘫,右大脚趾有1年病程的营养性溃疡。他自出生以来颈椎就有先天性皮样窦。术中发现该窦与硬膜内囊肿相关,组织病理学检查证实为室管膜囊肿。本文介绍了该罕见疾病的临床特征及相关文献回顾。