Nicola Zelletta, Antonio Calace, De Tommasi Antonio
Dipartimento di Neurochirurgia, Università degli Studi di Bari, Piazzale Giulio Cesare, Bari, 70124, Italy,
Eur Spine J. 2014 May;23 Suppl 2:192-6. doi: 10.1007/s00586-013-2930-2. Epub 2013 Aug 3.
Dermal sinus tract (DST) is an uncommon spinal dysraphism presenting in childhood along the midline neuroaxis. Cervical DST less frequent is in association with intramedullary abscess.
A 9-month-old baby was admitted to our unit suffering from right hemiparesis. Physical examination showed a cervical midline cutaneous fistula dripping a yellowish thick liquid. Cervical MRI showed at C5 level a sinus tract in continuity with a C3-C6 intramedullary lesion. Total removal of the fistula and the intramedullary lesion was performed. Histopathological examination confirmed the diagnosis of dermal sinus and abscess.
Post-operative cervical MRI showed a complete removal of the spinal dysraphism, fistula, and intramedullary abscess. The baby showed a progressive clinical improvement and was discharged on day 10 post-surgery.
Literature review confirms that an early diagnosis followed by prompt surgical spinal cord decompression gives a functional neurological recovery.
皮样窦道(DST)是一种罕见的脊髓发育异常,在儿童期沿中线神经轴出现。颈段皮样窦道较少见,常与髓内脓肿相关。
一名9个月大的婴儿因右侧偏瘫入住我院。体格检查发现颈部中线皮肤瘘管有淡黄色浓稠液体渗出。颈椎磁共振成像(MRI)显示在C5水平有一个窦道与C3 - C6髓内病变相连。对瘘管和髓内病变进行了完整切除。组织病理学检查确诊为皮样窦和脓肿。
术后颈椎MRI显示脊髓发育异常、瘘管和髓内脓肿已完全切除。婴儿临床症状逐渐改善,术后第10天出院。
文献综述证实,早期诊断并及时进行脊髓减压手术可实现神经功能恢复。