Brown John W, Rodefeld Mark D, Ruzmetov Mark
Section of Cardiothoracic Surgery, Indiana University School of Medicine, Indianapolis, IN, USA.
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu. 2009:66-9. doi: 10.1053/j.pcsu.2009.01.024.
Transverse aortic arch hypoplasia involving some or all segments of the arch (tubular hypoplasia) may exist in association with intra-cardiac anomalies of varying severity. Surgical repair of the distal transverse aortic arch and isthmus are adequately managed by an extended end-to-end coarctation repair in most infants via a left thoracotomy. The surgical management and timing of proximal aortic arch obstruction is controversial but almost always requires an approach via sternotomy using cardiopulmonary bypass.
涉及主动脉弓部分或全部节段的横断主动脉弓发育不全(管状发育不全)可能与不同严重程度的心脏内异常并存。对于大多数婴儿,通过左胸切口进行的扩大端端缩窄修复术可充分处理远端横断主动脉弓和峡部的手术修复。近端主动脉弓梗阻的手术处理和时机存在争议,但几乎总是需要通过胸骨切开术并使用体外循环的方法。