Onitsuka T, Nakamura K, Kuwabara M, Yonezawa T, Shibata K, Koga Y
Second Department of Surgery, Miyazaki Medical College, Japan.
Nihon Kyobu Geka Gakkai Zasshi. 1991 Aug;39(8):1184-7.
A 51-year-old woman was admitted with increasing shortness of breath. Preoperative evaluation disclosed MSr + ASr + TR. She had been undergone a splenectomy at 35-year-old for hereditary spherocytosis (HS). The patient underwent successful mitral valve replacement with a No. 25 Björk-Shiley (BS) valve, aortic valve replacement with a No. 21 BS valve, and tricuspid valve annuloplasty by means of membrane oxygenator (COBE). Haptoglobin and poloxamer 188 were used for prevention of hemolysis during extracorporeal circulation. No significant hemolysis occurred intra-or postoperatively. A very rare case of open heart surgery associated with HS was reported.
一名51岁女性因气短加重入院。术前评估显示二尖瓣狭窄+主动脉瓣狭窄+三尖瓣反流。她35岁时因遗传性球形红细胞增多症(HS)接受了脾切除术。患者成功接受了二尖瓣置换术,使用25号Björk-Shiley(BS)瓣膜;主动脉瓣置换术,使用21号BS瓣膜;并通过膜式氧合器(COBE)进行了三尖瓣环成形术。在体外循环期间,使用了触珠蛋白和泊洛沙姆188预防溶血。术中及术后均未发生明显溶血。报道了一例与HS相关的非常罕见的心脏直视手术病例。