Tsolakis Ioannis, Lampropoulos George, Zolota Vassiliki, Papadoulas Spyros, Christeas Nikolaos
Department of Vascular Surgery, University Hospital of Patras, Rion, Greece.
Vascular. 2009 May-Jun;17(3):176-80. doi: 10.2310/6670.2008.00078.
Primary aortic tumors are rare and include a variety of histologic types, including aortic angiosarcomas, with less than 100 cases being reported since the first description of these tumors in 1873. The diagnosis of aortic angiosarcoma is usually confirmed by postoperative histopathologic examination or postmortem study. We present a case of primary aortic angiosarcoma presenting with intermittent claudication and radiologic findings of aortoiliac atherosclerotic disease treated initially with stenting; lower extremity embolic skin metastases developed during follow-up that prompted resection of the aortic bifurcation and restoration of the arterial continuity with a bypass. Despite postresection recurrence, a 3-year survival was achieved with aggressive multidisciplinary management.
原发性主动脉肿瘤罕见，包括多种组织学类型，如主动脉血管肉瘤，自1873年首次描述这些肿瘤以来，报告的病例不足100例。主动脉血管肉瘤的诊断通常通过术后组织病理学检查或尸检研究来确诊。我们报告一例原发性主动脉血管肉瘤病例，患者表现为间歇性跛行，影像学检查显示腹主动脉-髂动脉粥样硬化性疾病，最初接受了支架置入治疗；随访期间出现下肢栓塞性皮肤转移，促使切除主动脉分叉并通过旁路手术恢复动脉连续性。尽管切除术后复发，但通过积极的多学科管理实现了3年生存期。
