Pérez Margarita, Ruiz Jonatan R, Fernández Del Valle María, Nogales-Gadea Gisela, Andreu Antoni L, Arenas Joaquín, Lucía Alejandro
Universidad Europea de Madrid (Polideportivo), 28670 Villaviciosa de Odón, Madrid, Spain.
Neuromuscul Disord. 2009 Jun;19(6):403-5. doi: 10.1016/j.nmd.2009.04.010. Epub 2009 May 27.
We investigated the phenomenon of second wind in four patients with McArdle's disease: a brother and sister (aged 4 and 12 years respectively) and two unrelated patients, a boy of 14 and a 17-year-old girl. We also studied the siblings' healthy 6-year-old sister. Each patient performed a 15-min exercise test at a constant workload and a subsequent graded exercise test until exhaustion. Overall the healthy girl and the youngest McArdle's patient, the 4-year-old boy, did not show a second wind phenomenon. Further, the peak cardio-respiratory capacity of the young McArdle's boy was normal for his age (32.3 mL 02/kg/min) and he did not report any function limitations during physical education classes.
我们对四名患有麦克尔迪氏病的患者的“第二次呼吸”现象进行了研究：一对兄妹（分别为4岁和12岁）以及另外两名无亲属关系的患者，一名14岁男孩和一名17岁女孩。我们还研究了这对兄妹健康的6岁妹妹。每位患者均在恒定工作量下进行了15分钟的运动测试，随后进行分级运动测试直至精疲力竭。总体而言，健康女孩和最年幼的麦克尔迪氏病患者，即4岁男孩，未表现出“第二次呼吸”现象。此外，年幼的麦克尔迪氏病男孩的心肺功能峰值对于其年龄来说是正常的（32.3毫升氧气/千克/分钟），并且他在体育课上未报告任何功能受限情况。
