Kakizoe Manabu, Takizawa Akitoshi, Hattori Yusuke, Teranishi Junichi, Kondou Keiichi, Kishida Takeshi, Saitou Kazuo, Noguchi Kazumi, Kubota Yoshinobu, Murakami Ayumi, Sasaki Takeshi
Department of Urology and Renal Transplantation, Yokohama City University Medical Center.
Hinyokika Kiyo. 2009 May;55(5):249-52.
We report a 44-year-old female with lymphangiomyomatosis (LAM) of the kidney and retroperitoneum. Abdominal ultrasonography revealed a right kidney tumor, and she was referred to our department. Computed tomography (CT) revealed a para-aortic phyma in addition to the tumor. We performed retroperitoneal tumorectomy and partial resection of the right kidney via laparotomy. Pathological findings suggested LAM. LAM usually induces pulmonary lesions and its prognosis is relatively unfavorable. Female hormones are considered to be involved in the aggravation of LAM. The lesion may not have reached the lung in this postmenopausal woman because of the absence of these hormones.
我们报告一例44岁患有肾及腹膜后淋巴管平滑肌瘤病（LAM）的女性患者。腹部超声检查发现右肾肿瘤，遂转诊至我科。计算机断层扫描（CT）显示除肿瘤外，腹主动脉旁有一肿块。我们通过剖腹手术进行了腹膜后肿瘤切除术及右肾部分切除术。病理检查结果提示为LAM。LAM通常会引发肺部病变，其预后相对较差。女性激素被认为与LAM的病情加重有关。由于该绝经后女性缺乏这些激素，病变可能尚未累及肺部。
