Kehagias D, Pafiti A, Vaos N, Samanidis L
Department of Radiology, University of Athens, Areteion Hospital, 76 Vas. Sophias Av., Athens 115 28, Greece.
Eur Radiol. 1998;8(3):471-3. doi: 10.1007/s003300050417.
Lymphangioleiomyomatosis is a rare disease involving the lung, lymphatic trunk and lymph nodes. Sometimes it appears in the retroperitoneum with or without subsequent development in the lungs. We present a 52-year-old woman with retroperitoneal location of the disease. We discuss the abdominal CT appearance, the cytologic and immunophenotypic features and a preoperative differential diagnosis is attempted.
淋巴管平滑肌瘤病是一种累及肺、淋巴干和淋巴结的罕见疾病。有时它出现在腹膜后，可伴有或不伴有随后肺部的病变。我们报告一名52岁患有腹膜后淋巴管平滑肌瘤病的女性。我们讨论了腹部CT表现、细胞学和免疫表型特征，并尝试进行术前鉴别诊断。
