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复发性左房葡萄状横纹肌肉瘤

Recurrent Left Atrial Botyroid Rhabdomyosarcoma.

作者信息

Abay Günseli, Kocaaslan Cemal, Günay Rafet, Doğan Meryem, Demirtaş Mahmut Murat

机构信息

Department of Anesthesiology, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Center, Istanbul, Turkey.

Department of Cardiovascular Surgery, Dr. Siyami Ersek Thoracic and Cardiovascular Surgery Center, Istanbul, Turkey.

出版信息

Heart Surg Forum. 2016 May 9;19(3):E097-8. doi: 10.1532/hsf.1418.

Abstract

Primary heart tumors are extremely rare and their frequency ranges from approximately 0.01-0.3% in autopsy series. Nearly one quarter of all primary cardiac tumors are malignant tumors such as sarcoma. Rhabdomyosarcoma is the second most common malignant primary tumor of the heart following angiosarcoma.Primary cardiac tumors present with one or more of the symptoms of the classic triad: cardiac symptoms and signs resulting from intracardiac obstruction; signs of systemic embolization; and systemic or constitutional symptoms. The prognosis after surgery is usually excellent in case of benign tumors, but is unfortunately still limited in localized malignant diseases [Butany 2005].In this case report we present a 45-year-old female patient operated three times in 9 years because of left atrial tumor.

摘要

原发性心脏肿瘤极为罕见,在尸检系列中的发生率约为0.01%-0.3%。所有原发性心脏肿瘤中近四分之一是恶性肿瘤,如肉瘤。横纹肌肉瘤是仅次于血管肉瘤的第二常见的原发性心脏恶性肿瘤。原发性心脏肿瘤表现为典型三联征中的一种或多种症状:心内梗阻导致的心脏症状和体征;全身栓塞的体征;以及全身或全身症状。良性肿瘤手术后的预后通常良好,但不幸的是,局限性恶性疾病的预后仍然有限[布塔尼,2005年]。在本病例报告中,我们介绍了一名45岁的女性患者,因左心房肿瘤在9年内接受了三次手术。

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