伴有完全性尿道重复的膀胱外翻-尿道上裂复合畸形：术前诊断必不可少。

Exstrophy-epispadias complex associated with complete urethral duplication: preoperative diagnosis is a must.

机构信息

Department of Pediatric Surgery and Urology, AP-HP, Robert Debré University Hospital, University of Paris VII, Paris, France.

出版信息

Urology. 2009 Dec;74(6):1228-9. doi: 10.1016/j.urology.2009.05.022. Epub 2009 Jul 17.

DOI:10.1016/j.urology.2009.05.022

PMID:19616283

Abstract

We report a rare association of complete urethral duplication and exstrophy-epispadias complex in a totally incontinent boy. A voiding cystourethrography was performed and revealed a dorsal epispadiac urethra, a normal ventral urethra, and a good bladder capacity. Urethrocystoscopy showed a normal ventral urethra with verumontanum, normal bladder neck, and a large opening of the dorsal urethra. Dorsal urethral excision and bladder closure were enough to achieve complete continence because of the normal ventral urethra.

摘要

我们报告了一例完全性尿道重复和脐尿管外翻-尿道上裂复合畸形的罕见病例，该患儿完全失禁。行排尿性膀胱尿道造影显示背侧尿道上裂，正常腹侧尿道和良好的膀胱容量。尿道膀胱镜检查显示正常的腹侧尿道有精阜，正常的膀胱颈部和较大的背侧尿道开口。由于有正常的腹侧尿道，因此行背侧尿道切除和膀胱关闭术足以实现完全控尿。