伴有H型肛门前庭瘘的 Mayer-Rokitansky-Kuster-Hauser综合征

Mayer-Rokitansky-Kuster-Hauser syndrome with H-type anovestibular fistula.

作者信息

Mahajan Jai Kumar, Venkatesh M A, Bawa Monika, Rao Katargadda L N

机构信息

Department of Pediatric Surgery, Advanced Pediatric Center, Postgraduate Institute of Medical Education and Research, Chandigarh 160012, India.

出版信息

J Pediatr Surg. 2009 Aug;44(8):E1-3. doi: 10.1016/j.jpedsurg.2009.04.015.

DOI:10.1016/j.jpedsurg.2009.04.015

PMID:19635284

Abstract

Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is characterized by Mullerian duct structures agenesis. Anorectal malformations are uncommonly associated with MRKH syndrome, and among them, rectovestibular fistula and cloacal malformations have been commonly described. H-type of anovestibular fistula associated with MRKH syndrome has not been reported previously. One such case along with its treatment is reported.

摘要

迈耶-罗基坦斯基-库斯特-豪泽（MRKH）综合征的特征是苗勒管结构发育不全。肛门直肠畸形与MRKH综合征的关联并不常见，其中，直肠前庭瘘和泄殖腔畸形较为常见。此前尚未报道过与MRKH综合征相关的H型肛门前庭瘘。本文报告了这样一例病例及其治疗情况。