Rampone B, Filippeschi M, Di Martino M, Marrelli D, Pedrazzani C, Grimaldi L, Cerullo G, Caruso S, Pinto E, Roviello F
Department of General Surgery and Surgical Oncology, University of Siena, Siena, Italy.
G Chir. 2008 Apr;29(4):165-7.
Mayer-Rokitansky-Küster-Hauser syndrome (MRKH syndrome) is characterized by Müllerian duct structures agenesis: the vagina atresia is the commonest variant. There can be some anomalies associated, such as renal, skeletal, spine malformations and others. Patients with MRKH can show different presentation from newborn period to adolescence. We report our experience in treatment of the vaginal atresia presenting in two young girls as a sign of MRKH syndrome.
迈耶-罗基坦斯基-库斯特-豪泽综合征（MRKH综合征）的特征是苗勒管结构发育不全：阴道闭锁是最常见的变异类型。可能还会伴有一些异常情况，如肾脏、骨骼、脊柱畸形等。MRKH综合征患者从新生儿期到青春期会有不同的表现。我们报告了我们治疗两名年轻女孩阴道闭锁（作为MRKH综合征的一种表现）的经验。
