Doorenbosch Xenia, Santoreneos Stephen, Molloy Cindy J, David David J, Anderson Peter J
Department of Neurosurgery, Women's and Children's Hospital, North Adelaide, South Australia 5006, Australia.
Childs Nerv Syst. 2009 Nov;25(11):1481-3. doi: 10.1007/s00381-009-0955-y. Epub 2009 Jul 31.
Chordomas are rare slow growing, locally destructive tumours originating from remnants of the primitive notocord and are found most commonly in the clivus and saccrococcygeal region. These tumours usually present in early adult life but on occasion can present in childhood. The combination of the skull base location and paediatric patient size makes access to these tumours particularly challenging.
We report a multidisciplinary technique used in two cases in children where a modified extended palatal split was undertaken to allow greater access for tumour excision.
This approach allows for good access to the skull base region to allow for maximal tumour resection. This technique also appears to have minimal impact on palatal function and no adverse effects on the upper airway management.
脊索瘤是一种罕见的、生长缓慢、具有局部破坏性的肿瘤，起源于原始脊索的残余部分，最常见于斜坡和骶尾部区域。这些肿瘤通常在成年早期出现，但偶尔也会在儿童期出现。颅底位置和儿科患者体型的结合使得切除这些肿瘤极具挑战性。
我们报告了一种多学科技术，该技术用于两例儿童患者，采用改良的扩大腭部劈开术以获得更大的肿瘤切除空间。
这种方法能够很好地进入颅底区域，以实现最大程度的肿瘤切除。该技术似乎对腭部功能影响最小，对上气道管理也无不良影响。
