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The regulation of sterol biosynthesis in leucocytes of subjects with familial hypercholesterolaemia.

作者信息

Higgins M J, Galton D J

出版信息

Eur J Clin Invest. 1977 Aug;7(4):301-5. doi: 10.1111/j.1365-2362.1977.tb01609.x.

DOI:10.1111/j.1365-2362.1977.tb01609.x
PMID:196863
Abstract
摘要

相似文献

1
The regulation of sterol biosynthesis in leucocytes of subjects with familial hypercholesterolaemia.
Eur J Clin Invest. 1977 Aug;7(4):301-5. doi: 10.1111/j.1365-2362.1977.tb01609.x.
2
A new type of familial hypercholesterolaemia.
Lancet. 1975 Oct 18;2(7938):737-40. doi: 10.1016/s0140-6736(75)90723-0.
3
Properties of sterol biosynthesis in human leukocytes: effects of gemfibrozil.人白细胞中甾醇生物合成的特性:吉非贝齐的作用
Proc R Soc Med. 1976;69 Suppl 2(Suppl 2):104-6. doi: 10.1177/00359157760690S227.
4
Decreased cholesterol biosynthesis in sitosterolemia with xanthomatosis: diminished mononuclear leukocyte 3-hydroxy-3-methylglutaryl coenzyme A reductase activity and enzyme protein associated with increased low-density lipoprotein receptor function.伴有黄色瘤病的谷甾醇血症中胆固醇生物合成减少:单核白细胞3-羟基-3-甲基戊二酰辅酶A还原酶活性及酶蛋白降低,同时低密度脂蛋白受体功能增强。
Metabolism. 1990 Apr;39(4):436-43. doi: 10.1016/0026-0495(90)90260-j.
5
Control of lipid metabolism in human leukocytes.人类白细胞中脂质代谢的调控
J Biol Chem. 1973 Oct 10;248(19):6828-9.
6
Regulation of cholesterol synthesis in the hyperlipoproteinaemias. Polymorphonuclear leucocyte abnormality specific to familial type II hypercholesterolaemia.高脂血症中胆固醇合成的调节。家族性II型高胆固醇血症特有的多形核白细胞异常。
Atherosclerosis. 1978 Mar;29(3):291-9. doi: 10.1016/0021-9150(78)90077-1.
7
Regulation of sterol synthesis in leukaemic blast cells: a defect resembling familial hypercholesterolaemia.白血病原始细胞中固醇合成的调节:一种类似于家族性高胆固醇血症的缺陷。
Eur J Clin Invest. 1979 Dec;9(6):439-41. doi: 10.1111/j.1365-2362.1979.tb00909.x.
8
Regulation of 3-hydroxy-3-methylglutaryl coenzyme-A reductase activity in type II hyperlipoproteinaemia.II型高脂蛋白血症中3-羟基-3-甲基戊二酰辅酶A还原酶活性的调节
Br Med J. 1975 Nov 29;4(5995):500-2. doi: 10.1136/bmj.4.5995.500.
9
Evidence for rate-limiting steps in sterol synthesis beyond 3-hydroxy-3-methylglutaryl-coenzyme A reductase in human leukocytes.
Biochim Biophys Acta. 1979 Feb 26;572(2):345-51. doi: 10.1016/0005-2760(79)90050-x.
10
The regulation of cholesterol synthesis in human cells.人体细胞中胆固醇合成的调节
Int J Obes. 1981;5(6):619-25.

引用本文的文献

1
In vivo regulation of human mononuclear leukocyte 3-hydroxy-3-methylglutaryl coenzyme A reductase. Decreased enzyme catalytic efficiency in familial hypercholesterolemia.人单核白细胞3-羟基-3-甲基戊二酰辅酶A还原酶的体内调节。家族性高胆固醇血症中酶催化效率降低。
J Clin Invest. 1987 Nov;80(5):1401-8. doi: 10.1172/JCI113218.
2
Diagnosing familial hypercholesterolaemia in childhood.儿童家族性高胆固醇血症的诊断
Br Med J. 1977 Oct 29;2(6095):1156. doi: 10.1136/bmj.2.6095.1156.
3
A new simple assay for total blood lipids by refractometry.一种通过折射法测定全血脂质的新型简易检测方法。
Experientia. 1979 Mar 15;35(3):424-5. doi: 10.1007/BF01964389.