Carpentier Heather, Maizlin Ilan, Bliss David
School of Medicine, Oregon Health & Science University, 3181 SW Sam Jackson Park Road, Portland, OR 97239-3098, USA.
Pediatr Surg Int. 2009 Oct;25(10):911-6. doi: 10.1007/s00383-009-2474-z.
Anal canal duplication (ACD) is a rare entity that is difficult to recognize. After the presentation of two patients, a review of the literature found 45 reported patients with ACD. This article presents the largest collection of known patients ACD in the literature. Of the 47 patients, 43 were female. The mean age at presentation was 28 months (range 0-24 years). The majority of the duplications were discovered incidentally (n = 21). Several presented with infectious complications such as epidural abscess with sepsis. Forty-two patients manifested an opening in the midline posterior to the native anus. Eighteen patients had associated anomalies, the majority of which were midline. Thirty-five of the patients underwent successful resection with rare complications. ACDs characteristically appear in females as incidental findings of an extra perineal orifice. They are frequently associated with additional congenital anomalies. Generally, ACDs are resectable with excellent outcomes.
肛管重复畸形（ACD）是一种罕见且难以识别的疾病。在介绍了两名患者后，通过文献回顾发现了45例已报道的ACD患者。本文展示了文献中已知的最大规模的ACD患者群体。在这47例患者中，43例为女性。就诊时的平均年龄为28个月（范围0至24岁）。大多数重复畸形是偶然发现的（n = 21）。有几例出现了感染性并发症，如伴有败血症的硬膜外脓肿。42例患者在原生肛门后方的中线处有开口。18例患者伴有相关异常，其中大多数为中线异常。35例患者成功接受了切除手术，并发症罕见。ACD在女性中通常表现为会阴外口的偶然发现。它们常与其他先天性异常相关。一般来说，ACD可通过手术切除，效果良好。
