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不一致双胎之一出现“增大的”胎粪囊肿:一例报告

"Growing" meconium cyst in one of a discordant twin: a case report.

作者信息

Abdulkadir Adekunle Y, Abdur-Rahman Lukman O

机构信息

Department of Radiology, University of Ilorin Teaching Hospital, Ilorin, Kwara State Nigeria.

出版信息

Cases J. 2009 May 14;2:7008. doi: 10.1186/1757-1626-2-7008.

DOI:10.1186/1757-1626-2-7008
PMID:19829894
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2740019/
Abstract

INTRODUCTION

Giant meconium cyst resulting from antenatal bowel perforation is rare and hardly reported in multiple gestations. We found only four documented cases in the electronic literature.

CASE PRESENTATION

We report a giant meconium cyst in an 11-hour-old Nigerian boy of a discordant twin having ultrasonographic and plain radiographic diagnosis and surgical confirmation. Increasing abdominal girth from 35 cm to 41 cm within four hours of admission without ascites, pneumoperitneum and significant bowel distension make us assumed the meconium cyst to be "growing" in size. We reviewed the literature and proposed that where the fibrinous wall of meconium cyst allows for distensibility and the communication between the perforated bowel and meconium cyst persists, the meconium cyst acting as reservoir may continue to "grow" in size without remarkable intestinal distension probably, until the elastic limit is lost.

CONCLUSION

Meconium cyst can occur in twin pregnancy, grow to occupy the abdomen almost completely and may cause neonatal apnoea. The outcome is good post surgery.

摘要

引言

产前肠穿孔导致的巨大胎粪囊肿罕见,在多胎妊娠中鲜有报道。我们在电子文献中仅发现4例有记录的病例。

病例报告

我们报告一例巨大胎粪囊肿,患儿为一名11小时大的尼日利亚男婴,是双绒毛膜双胎中的不一致胎儿,经超声和X线平片诊断,并经手术证实。入院后4小时内腹围从35厘米增加到41厘米,无腹水、气腹及明显肠扩张,这使我们推测胎粪囊肿在“长大”。我们回顾文献并提出,若胎粪囊肿的纤维壁具有可扩张性且穿孔肠管与胎粪囊肿之间的通道持续存在,作为储存库的胎粪囊肿可能会继续“长大”,且可能不会出现明显的肠扩张,直到失去弹性限度。

结论

胎粪囊肿可发生于双胎妊娠,可长大至几乎完全占据腹部,并可能导致新生儿呼吸暂停。手术效果良好。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28be/2740019/2073990025b2/1757-1626-0002-0000007008-003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28be/2740019/3ce986db28c0/1757-1626-0002-0000007008-001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28be/2740019/01405785bf23/1757-1626-0002-0000007008-002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28be/2740019/2073990025b2/1757-1626-0002-0000007008-003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28be/2740019/3ce986db28c0/1757-1626-0002-0000007008-001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28be/2740019/01405785bf23/1757-1626-0002-0000007008-002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/28be/2740019/2073990025b2/1757-1626-0002-0000007008-003.jpg

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Prenatal MR imaging of a meconium pseudocyst extending to the right subphrenic space with right lung compression.产前磁共振成像显示胎粪假性囊肿延伸至右膈下间隙并压迫右肺。
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Arch Gynecol Obstet. 2002 Aug;266(4):229-31. doi: 10.1007/s004040100218.
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Prenatal diagnosis of meconium peritonitis in a twin pregnancy after intracytoplasmic sperm injection. A case report.胞浆内单精子注射后双胎妊娠中胎粪性腹膜炎的产前诊断。病例报告。
J Reprod Med. 2000 Nov;45(11):953-6.
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J Pediatr Surg. 1995 Jul;30(7):979-82. doi: 10.1016/0022-3468(95)90325-9.
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Cystic meconium peritonitis: ultrasonographic features.胎粪性腹膜炎:超声特征
Pediatr Radiol. 1984;14(1):18-22. doi: 10.1007/BF02386725.
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Radiographic diagnosis of meconium peritonitis. A report of 200 cases including six fetal cases.胎粪性腹膜炎的影像学诊断。200例报告,其中包括6例胎儿病例。
Pediatr Radiol. 1983;13(4):199-205. doi: 10.1007/BF00973156.
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Meconium peritonitis presenting as giant cysts in neonates.
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