Xin Long, Tian Zheng, Fan Shunwu
Orthopaedic Laboratory, Clinic Medical Research Institution, Sir Run Run Shaw Hospital, Zhejiang University School of Medicine,NO.3 Qingchun Road, Hangzhou, 310016, Zhejiang Province, China.
Cases J. 2009 Jun 10;2:7499. doi: 10.4076/1757-1626-2-7499.
The Gorham-Stout Syndrome (Gorham's massive osteolysis) is a rare condition in which spontaneous, progressive resorption of bone occurs. The etiology is poorly understood.
We reported here a patient who had begun insidiously and was characterized by extensive osteolysis in the left upper limb, with progressive carpal bone resorption. The characteristic radiological and CT findings were presented and the clinical presentation, diagnosis and surgical treatment were discussed in the case.
Gorham's disease is rarely involved in the whole upper limb. Histopathological evidences suggest that extensive osteolysis is caused by hemangiomatosis. The characteristic imaging findings may help us to differentiate from malignant neoplasm with progressive bony destruction.
戈勒姆-斯托特综合征（戈勒姆氏大块骨质溶解症）是一种罕见病症，其中会发生骨骼的自发性、进行性吸收。其病因尚不清楚。
我们在此报告一名患者，其起病隐匿，特征为左上肢广泛骨质溶解，并伴有腕骨进行性吸收。文中展示了该病例的特征性放射学和CT表现，并讨论了临床表现、诊断及外科治疗。
戈勒姆病很少累及整个上肢。组织病理学证据表明，广泛骨质溶解是由血管瘤病引起的。特征性影像学表现可能有助于我们将其与伴有进行性骨质破坏的恶性肿瘤相鉴别。
