Brock Macy, Guinn Cherry, Jones Monica
University of Tennessee at Chattanooga/Erlanger Health System, Nurse Anesthesia Concentration, USA.
AANA J. 2009 Oct;77(5):335-7.
Additional documentation of regional anesthesia in patients with Charcot-Marie-Tooth disease (CMT) is needed to guide practitioners and patients in exploring appropriate options for anesthesia and analgesia management. This case report describes the successful use of a combined spinal-epidural technique for labor progressing to cesarean delivery in a patient with CMT. Previous similar case reports were reviewed and an extensive literature search was conducted to organize the limited body of research regarding use of regional anesthesia in patients with CMT. Opinions regarding regional anesthesia in patients with neuromuscular diseases such as CMT are often contradictory and based on theory rather than documented practice. This case report confirms what seems to be the developing consensus in anesthesia that regional management is a safe alternative to general anesthesia in these patients. Considering that CMT is among the most common of hereditary neuromuscular diseases, it seems valid to establish a more research-driven recommendation for practice.
需要更多关于夏科-马里-图斯病（CMT）患者区域麻醉的文献资料，以指导从业者和患者探索麻醉和镇痛管理的合适方案。本病例报告描述了一名CMT患者成功使用腰麻-硬膜外联合技术进行剖宫产的过程。回顾了以前类似的病例报告，并进行了广泛的文献检索，以整理关于CMT患者使用区域麻醉的有限研究。对于CMT等神经肌肉疾病患者的区域麻醉，观点往往相互矛盾，且基于理论而非实际记录。本病例报告证实了麻醉领域似乎正在形成的共识，即区域管理是这些患者全身麻醉的安全替代方案。鉴于CMT是最常见的遗传性神经肌肉疾病之一，建立一个更以研究为导向的实践建议似乎是合理的。
