Department of Radiology, University of California San Francisco, San Francisco, CA 94143-0628, USA.
Pediatr Radiol. 2010 Mar;40(3):358-60. doi: 10.1007/s00247-009-1454-8.
Uterine didelphys with obstructed hemivagina and ipsilateral renal anomalies is a rare congenital malformation of the female urogenital tract. While the urinary anomalies almost always involve renal agenesis, we report a rare case of a 17-year-old girl with the malformation associated with ectopic ureteral insertion into the obstructed hemivagina, which was diagnosed preoperatively by MR imaging. To the best of our knowledge, preoperative MR imaging diagnosis of the ectopic ureter associated with this syndrome has not been previously reported. Accurate preoperative diagnosis of ectopic ureteral insertion associated with this syndrome is important for surgical planning.
子宫双角畸形伴同侧半侧阴道闭锁和肾发育不全是一种罕见的女性生殖道先天性畸形。虽然泌尿系统异常几乎总是涉及肾发育不全，但我们报告了一例罕见的 17 岁女孩，该畸形伴有异位输尿管插入梗阻性半侧阴道，术前通过磁共振成像（MR 成像）诊断。据我们所知，术前 MR 成像诊断该综合征相关的异位输尿管尚未见报道。准确术前诊断该综合征相关的异位输尿管插入对于手术计划非常重要。
