Lee Hyun, Cho Jeong Yeon, Kim Seung Hyup, Jung Dae Chul, Kim Jeong Kon, Choi Hyuk Jae
Department of Radiology, Hallym University Sacred Heart Hospital, Seoul, Republic of Korea.
J Comput Assist Tomogr. 2009 Nov-Dec;33(6):882-6. doi: 10.1097/RCT.0b013e31819e938b.
This study was designed to present the radiological imaging findings of a renal primitive neuroectodermal tumor (PNET).
The study included 10 patients with pathologically proven renal PNETs. We assessed the size, margin, internal architecture, enhancement pattern, vein thrombosis, and presence of a metastasis of the tumors on multidetector-row computed tomography and magnetic resonance imaging.
The mean age of the patients was 31 years. Patients were predominantly male (males-females, 8:2). The mean diameter of a renal PNET was 12.7 cm. All masses were well defined with a lobulated contour. Necrosis and hemorrhage were detected in 9 cases, respectively. All of the masses showed weak heterogeneous enhancement with multiple irregular septumlike structures. Eight of the masses had renal vein thrombosis, and 4 masses had extension into inferior vena cava. A lymph node metastasis was detected in 3 patients. A lung metastasis was detected in 4 patients, and 2 of the patients also had a bone metastasis.
A renal PNET usually appears as a weakly enhanced large mass with multiple septumlike structures, peripheral hemorrhage, venous thrombosis, and accompanied with a distant metastasis in a young adult.
本研究旨在呈现肾原始神经外胚层肿瘤（PNET）的放射影像学表现。
本研究纳入10例经病理证实的肾PNET患者。我们在多排螺旋计算机断层扫描和磁共振成像上评估了肿瘤的大小、边缘、内部结构、强化方式、静脉血栓形成以及转移情况。
患者的平均年龄为31岁。患者以男性为主（男∶女 = 8∶2）。肾PNET的平均直径为12.7 cm。所有肿块边界清晰，轮廓呈分叶状。分别在9例中检测到坏死和出血。所有肿块均表现为不均匀轻度强化，伴有多个不规则的分隔样结构。8例肿块有肾静脉血栓形成，4例肿块延伸至下腔静脉。3例患者检测到淋巴结转移。4例患者检测到肺转移，其中2例患者还伴有骨转移。
肾PNET在年轻成人中通常表现为强化较弱的大肿块，伴有多个分隔样结构、周边出血、静脉血栓形成，并伴有远处转移。
