Division of Plastic and Reconstructive Surgery, Hospital Santa Casa da Misericórdia do Rio de Janeiro.
Aesthet Surg J. 2009 Nov-Dec;29(6):494-504. doi: 10.1016/j.asj.2009.09.015.
Many chest wall deformities have a characteristic radiologic appearance that can be the basis for a definitive diagnosis. Consequently, imaging techniques have fundamental roles in the detection, location, and characterization of these disorders.
The authors propose a clinical and radiographic Poland syndrome (CRPS) classification system and possible treatment algorithm for the thoracic manifestations of Poland syndrome (PS) in women, based on both clinical examinations and imaging studies.
A retrospective study was conducted of 28 female patients evaluated over 17 years in the 28th Infirmary, Plastic and Reconstructive Surgery Division of the Hospital Santa Casa da Misericórdia do Rio de Janeiro, Rio de Janeiro, Brazil. After clinical examination, all patients underwent radiographic examination with chest radiographs, conventional computed tomography scans, magnetic resonance imaging and, in some cases, additional imaging studies. All clinical and radiologic variables were compiled in a database and used in the classification system, which included three levels of disease severity.
Based on the CRPS classification of the 28 female patients, 10 patients had first-degree PS, 14 patients had second-degree PS, and four patients had third-degree PS. Eighteen patients underwent surgical correction; a total of 39 surgical procedures were performed using the CRPS algorithm.
Identification of the severity of PS using the proposed classification system provided an accurate study of each patient and enabled better planning for the surgical correction of functional and aesthetic deformities.
许多胸壁畸形具有特征性的影像学表现，可作为明确诊断的基础。因此，影像学技术在这些疾病的检测、定位和特征描述中具有重要作用。
作者提出了一种基于临床和影像学的波兰综合征（CRPS）分类系统和可能的治疗算法，用于女性波兰综合征（PS）的胸壁表现，该系统基于临床检查和影像学研究。
回顾性分析了巴西里约热内卢圣家慈悲仁慈医院 28 号医务室整形与重建外科分部在 17 年内评估的 28 名女性患者。临床检查后，所有患者均行胸部 X 线片、常规 CT 扫描、磁共振成像检查，部分患者行额外影像学检查。所有临床和影像学变量均在数据库中进行编译，并用于包括疾病严重程度三个等级的分类系统中。
根据 28 名女性患者的 CRPS 分类，10 名患者为一级 PS，14 名患者为二级 PS，4 名患者为三级 PS。18 名患者接受了手术矫正；共根据 CRPS 算法进行了 39 次手术。
使用提出的分类系统确定 PS 的严重程度，可以对每位患者进行准确的研究，并为功能性和美容性畸形的手术矫正提供更好的规划。
