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[一例腹膜后黏液纤维肉瘤]

[A case of retroperitoneal myxofibrosarcoma].

作者信息

Takeda Ken, Uehara Michiru, Tei Norihide, Shimizu Kiyonori, Imazu Tetsuo, Yoshimura Kazuhiro, Kiyohara Hisakazu

机构信息

The Department of Urology, Toyonaka Municipal Hospital, Japan.

出版信息

Hinyokika Kiyo. 2009 Nov;55(11):711-4.

PMID:19946191
Abstract

A 63-year-old man presented to our hospital suffering from dull pain in his right flank and general malaise.Abdominal computed tomography (CT) revealed a 21X14 cm retroperitoneal tumor adjacent to the right kidney. He underwent extirpation of the tumor,which weighed 2,900 g. Histopathological diagnosis was high-grade myxofibrosarcoma. Six months after initial surgery,CT revealed isolated metastasis in the upper lobe of the left lung,which was surgically treated. Eleven months after the original tumor excision, CT revealed lymph node metastasis dorsal to the inferior vena cava,which was also removed. Because he refused to receive adjuvant chemotherapy,he was observed for 2 months until CT revealed multiple liver metastases and para-aortic lymph node metastasis. He underwent 1 cycle of combined chemotherapy with doxorubicin and carboplatin,but metastatic lesions grew larger rapidly and his general state became too poor to continue chemotherapy. He is under best supportive care 17 months after the initial surgery.

摘要

一名63岁男性因右侧胁腹钝痛和全身不适前来我院就诊。腹部计算机断层扫描(CT)显示右肾旁有一个21×14 cm的腹膜后肿瘤。他接受了肿瘤切除手术,肿瘤重2900 g。组织病理学诊断为高级别黏液纤维肉瘤。初次手术后6个月,CT显示左肺上叶孤立转移,遂行手术治疗。原发肿瘤切除术后11个月,CT显示下腔静脉背侧淋巴结转移,也予以切除。由于他拒绝接受辅助化疗,观察2个月后CT显示多发肝转移和主动脉旁淋巴结转移。他接受了1个周期的阿霉素和卡铂联合化疗,但转移病灶迅速增大,全身状况太差无法继续化疗。初次手术后17个月,他接受最佳支持治疗。

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