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泄殖腔存留的产前诊断。

Prenatal diagnosis of persistent cloaca.

作者信息

Suzumori Nobuhiro, Obayashi Shintaro, Hattori Yukio, Kaneko Saori, Suzuki Yoshikatsu, Sugiura-Ogasawara Mayumi

机构信息

Department of Obstetrics and Gynecology, Nagoya City University Graduate School of Medicine, Nagoya, Japan.

出版信息

Congenit Anom (Kyoto). 2009 Sep;49(3):116-7. doi: 10.1111/j.1741-4520.2009.00236.x.

Abstract

We report four cases of persistent cloaca diagnosed at 32-33 weeks of gestation. In cases of persistent cloaca, serial prenatal ultrasonography shows transient fetal ascites, enlarged cystic structures arising from the fetal pelvis. Our four cases of persistent cloaca were diagnosed prenatally. Persistent cloaca should be considered in any female fetus presenting with hydronephrosis and a large cystic lesion arising from the pelvis as assessed by ultrasound and magnetic resonance imaging. Neither pulmonary hypoplasia nor severe oligohydramnios were found in any of our four cases, and they each had a good prognosis. Prenatal diagnosis allows time for parental counseling and delivery planning at a tertiary care center for neonatal intensive care and pediatric surgery.

摘要

我们报告了4例在妊娠32 - 33周时诊断出的持续性泄殖腔畸形病例。在持续性泄殖腔畸形的病例中,系列产前超声检查显示短暂性胎儿腹水,以及源于胎儿骨盆的增大囊性结构。我们的4例持续性泄殖腔畸形病例均在产前被诊断出来。对于任何经超声和磁共振成像评估显示有肾盂积水以及源于骨盆的大囊性病变的女性胎儿,均应考虑持续性泄殖腔畸形的可能。我们的4例病例均未发现肺发育不全或严重羊水过少的情况,且预后均良好。产前诊断可为在三级医疗中心进行新生儿重症监护和小儿外科治疗的父母咨询及分娩计划争取时间。

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