Yonsei University College of Medicine, Seoul, Korea.
Rheumatol Int. 2012 Feb;32(2):479-82. doi: 10.1007/s00296-009-1259-y. Epub 2010 Jan 5.
Relapsing polychondritis (RP) is a rare disease which presents chondritis in multiple organs. Characteristic features include auricular chondritis, arthritis, nasal chondritis, ocular inflammation, respiratory tract involvement and audiovestibular damage. Fifty percent of cases of RP are associated with inner ear symptoms such as dizziness and hearing loss. We have recently encountered a case of RP in a 34-year-old man who had recurrent chondritis of both auricles and progressive bilateral profound sensorineural hearing loss; he had been treated many times with steroids, immunosuppressants, plasmapheresis treatments. We perfomed a successful cochlear implant surgery on the left ear of this patient. This raises the possibility of using cochlear implants in treating patients with immune-mediated inner ear disease as well as such RP patients.
复发性多软骨炎（RP）是一种罕见的疾病，其特征为多器官软骨炎。其特征性表现包括耳软骨炎、关节炎、鼻软骨炎、眼部炎症、呼吸道受累和听觉前庭损伤。50%的 RP 病例与内耳症状相关，如头晕和听力损失。我们最近遇到一例 34 岁男性 RP 患者，其双侧耳廓反复发作性软骨炎和进行性双侧深度感觉神经性听力损失；他曾多次接受类固醇、免疫抑制剂和血浆置换治疗。我们对该患者的左耳成功进行了耳蜗植入手术。这为治疗免疫介导性内耳疾病患者以及此类 RP 患者提供了使用耳蜗植入的可能性。
