儿童先天性颈椎后凸伴四肢轻瘫：病例报告

Congenital cervical kyphosis in a child associated with tetraparesis: case report.

作者信息

Van Gorp Viola, Dricot Frederic, van Berlaer Gerlant, Van Rompaey Katrijn, Hachimi-Idrissi Said

机构信息

Pediatric Critical Care Department, Universitair Ziekenhuis Brussel, BE-1090 Brussels, Belgium.

出版信息

Pediatr Neurosurg. 2009;45(6):422-4. doi: 10.1159/000270158. Epub 2009 Dec 24.

DOI:10.1159/000270158

PMID:20051702

Abstract

Congenital cervical kyphosis is a rare clinical condition. We describe an infant presenting with tetraparesis, rapidly progressing to phrenic paralysis and fatal respiratory insufficiency. Therapeutic options remain challenging. Surgical arthrodesis is technically difficult, and one report of a therapeutic thermoplastic body splint is described. Final outcome, however, is dismal. No long-term survivors have been described.

摘要

先天性颈椎后凸是一种罕见的临床病症。我们描述了一名出现四肢瘫痪的婴儿，其迅速发展为膈神经麻痹和致命的呼吸功能不全。治疗选择仍然具有挑战性。手术融合技术上难度较大，并且描述了一篇关于治疗性热塑性身体夹板的报告。然而，最终结果很糟糕。尚未有长期存活者的报道。