Department of Otolaryngology, The Royal Victorian Eye and Ear Hospital, East Melbourne, Victoria, Australia.
J Clin Neurosci. 2010 Mar;17(3):339-41. doi: 10.1016/j.jocn.2009.06.021. Epub 2010 Jan 13.
The aim of this study was to retrospectively review the clinical presentation, diagnostic features, in particular cervical vestibular evoked myogenic potentials (cVEMPs), and the outcomes of surgical repair for superior semicircular canal dehiscence syndrome (SSCDS). SSCDS is a well-described syndrome of auditory and vestibular symptoms due to a bony dehiscence of the superior semicircular canal in the middle cranial fossa. A series of six procedures on five patients with SSCDS who underwent surgical repair via a middle fossa craniotomy were retrospectively reviewed. Preoperative and postoperative audiometric and vestibular symptoms as well as investigation findings were reviewed. Auditory and vestibular symptoms improved and hearing was preserved in all patients. The low frequency pseudo-conductive loss was corrected in four out of five patients, and the lowered preoperative cVEMP thresholds normalised following successful middle cranial fossa repair. In this series, middle fossa repair of SSCD was safe and effective with excellent sensorineural hearing preservation.
本研究旨在回顾性分析上半规管裂综合征（SSCDS）的临床特征、诊断特点（特别是颈源性前庭诱发肌源性电位，cVEMPs）及手术修复的效果。SSCDS 是一种由于中颅窝上半规管骨质缺损导致的听觉和前庭症状的综合征。我们回顾性分析了 5 例接受经中颅窝颅底入路手术修复的 SSCDS 患者的 6 例手术。对患者的术前和术后听力和前庭症状及检查结果进行了评估。所有患者的听觉和前庭症状均得到改善，听力得以保留。5 例患者中有 4 例低频假性传导性听力损失得到纠正，且成功的中颅窝修复后，术前降低的 cVEMP 阈值恢复正常。在本研究中，经中颅窝修复 SSCD 安全有效，且能极好地保留感觉神经性听力。
