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一例罕见的分泌醛固酮的肾上腺皮质腺瘤伴发横纹肌溶解症。

An unusual case of an aldosterone-producing adrenocortical adenoma presenting with rhabdomyolysis.

作者信息

Karagüzel Gülay, Bahat Elif, Imamoğlu Mustafa, Ahmetoğlu Ali, Yildiz Kadriye, Okten Ayşenur

机构信息

Division of Pediatric Endocrinology, Department of Pediatrics, School of Medicine, Karadeniz Technical University, Trabzon, Turkey.

出版信息

J Pediatr Endocrinol Metab. 2009 Nov;22(11):1087-90. doi: 10.1515/jpem.2009.22.11.1087.

Abstract

Rhabdomyolysis is a rare presentation of hypokalemia, although muscle weakness is a well known manifestation of marked hypokalemia. Here, we report a case of primary hyperaldosteronism due to unilateral aldosterone-producing adenoma in a 14 year-old girl who developed rhabdomyolysis following hypokalemia. To our knowledge, this is the first case of adrenocortical adenoma presenting with rhabdomyolysis in a child.

摘要

横纹肌溶解症是低钾血症的一种罕见表现,尽管肌肉无力是显著低钾血症的一种众所周知的表现。在此,我们报告一例14岁女孩因单侧醛固酮分泌腺瘤导致原发性醛固酮增多症,该女孩在低钾血症后发生了横纹肌溶解症。据我们所知,这是儿童肾上腺皮质腺瘤伴横纹肌溶解症的首例病例。

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