Department of General Thoracic Surgery, Pathology, Mitsui Memorial Hospital, Tokyo, Japan.
Ann Thorac Surg. 2010 Jan;89(1):298-300. doi: 10.1016/j.athoracsur.2009.06.062.
Angiomyolipoma is generally found in the kidney, but is especially rare in the lung. Nine cases of angiomyolipoma in the lung have been reported previously, and in 3 of these patients it was involved with nephrectomy for renal angiomyolipoma. The origination of the tumor was not completely recognized, but lymphangioleiomyomatosis and angiomyolipoma are known to have a common feature. The pathogenesis of angiomyolipoma in the lung has recently been researched in relation with lymphangioleiomyomatosis. We review these case reports of angiomyolipoma in the lung and discuss the clinical features and the generation of these tumors.
血管平滑肌脂肪瘤通常发生在肾脏,但在肺部尤其罕见。此前已有 9 例肺部血管平滑肌脂肪瘤的报道,其中 3 例与肾血管平滑肌脂肪瘤的肾切除术有关。肿瘤的起源尚不完全清楚,但淋巴管平滑肌瘤病和血管平滑肌脂肪瘤具有共同的特征。最近,人们已经研究了与淋巴管平滑肌瘤病相关的肺部血管平滑肌脂肪瘤的发病机制。我们回顾了这些肺部血管平滑肌脂肪瘤的病例报告,并讨论了这些肿瘤的临床特征和发生机制。