Le Blanche A F, Pascaud J L, Bouillet P, Majoulet J F, Provensol T, Gaillard S
Service de Radiologie A, CHU Dupuytren, Limoges.
J Radiol. 1991 Jan;72(1):35-41.
We report two cases of Pulmonary Hemosiderosis. The first patient (adult male) had an angiosarcoma of the left auricle and developed pulmonary arterial hypertension, was treated by surgery and chemotherapy. The other patient (adult female) suffered from Idiopathic Pulmonary Hemosiderosis (IPH) and had been treated by corticosteroids for fifteen years, with one acute episode during this period. We discuss the etiological diagnosis and the contribution of chest radiographs, CT-scan and MR Imaging in this rare illness according to literature. IPH occurs mostly in childhood with acute and fatal issue, whereas presents as a chronic form in adults. Assessment of IPH requires large investigations to eliminate hemodynamic, hemato-, immuno-, carcinological disorders, and infectious agents as well. Review.
我们报告两例肺含铁血黄素沉着症。首例患者（成年男性）患有左心耳血管肉瘤并发展为肺动脉高压，接受了手术和化疗。另一例患者（成年女性）患有特发性肺含铁血黄素沉着症（IPH），接受皮质类固醇治疗已达十五年，在此期间有一次急性发作。我们根据文献讨论了这种罕见疾病的病因诊断以及胸部X光片、CT扫描和磁共振成像的作用。IPH大多发生于儿童期，病情急性且致命，而在成人中则表现为慢性形式。对IPH的评估需要进行大量检查以排除血液动力学、血液学、免疫学、肿瘤学疾病以及感染因素。综述。
