Pinto M, Correia J, Leal I, Reis A, Leão B, de Carvalho S, Sousa C S
Departamento de Medicina, Hospital Geral de Santo António, Porto.
Acta Med Port. 1996 Jan;9(1):41-4.
We report a case of a 23 year-old man admitted to hospital with cough, fever and recurrent episodes of haemoptysis. Laboratory findings, which included a pulmonary biopsy, established the diagnosis of Idiophatic Pulmonary Hemosiderosis (IPH). Despite a number of morphologic, immunologic and ultrastructural studies, the etiology and pathogenesis of this disease remain indetermined. To diagnose an IPH all the other causes of pulmonary hemorrhage must be excluded. This is a rare disease, even more rare in adults. Based on these facts the authors publish this article, which includes the case report and a literature review.
我们报告一例23岁男性患者,因咳嗽、发热和反复咯血入院。实验室检查结果,包括肺活检,确诊为特发性肺含铁血黄素沉着症(IPH)。尽管进行了多项形态学、免疫学和超微结构研究,但该疾病的病因和发病机制仍未明确。要诊断IPH,必须排除所有其他导致肺出血的原因。这是一种罕见疾病,在成年人中更为罕见。基于这些事实,作者发表了本文,其中包括病例报告和文献综述。