Ibrahim T M, Iheonunekwu N
Department of Medicine, Peebles Hospital, Pobox 439, Road Town, Tortola, British Virgin Islands.
Niger J Med. 2009 Oct-Dec;18(4):422-3. doi: 10.4314/njm.v18i4.51257.
Thrombotic thrombocytopenic purpura (TTP) is an uncommon and potentially fatal syndrome which is due to either congenital or acquired deficiency of the ultra large von Willbrand's factor (ULVWF) cleavage protease. It is characterized by mechanical micro angiopathic hemolytic anemia, and organ dysfunctions.
血栓性血小板减少性紫癜（TTP）是一种罕见且可能致命的综合征，其病因是超大型血管性血友病因子（ULVWF）裂解蛋白酶先天性或后天性缺乏。它的特征是机械性微血管病性溶血性贫血和器官功能障碍。
