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一例 Brugada 综合征伴无休止多形性室性心动过速。

A case of Brugada syndrome presenting with incessant polymorphic ventricular tachycardia.

机构信息

Section of Cardiology, Department of Medicine, Baylor College of Medicine, 1504 Taub Loop, Houston, TX 77030, USA.

出版信息

Clin Cardiol. 2010 Mar;33(3):E33-5. doi: 10.1002/clc.20641.

DOI:10.1002/clc.20641
PMID:20127895
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6652961/
Abstract

Brugada syndrome, an inherited arrhythmogenic cardiac disease, manifests with ST-segment changes in the right precordial leads, right bundle block pattern, and susceptibility to ventricular tachyarrhythmias and sudden death. The only established therapy for this disease is prevention of sudden death by implantation of a defibrillator. Herein we describe a case of a patient who presented with incessant ventricular tachycardia (VT) and syncope and who had a type 1 Brugada pattern on ECG. The patient was successfully treated with quinidine, after which the classically described type 2 and 3 patterns emerged.

摘要

Brugada 综合征是一种遗传性心律失常性心脏病,表现为右胸前导联 ST 段改变、右束支传导阻滞图形以及室性心动过速和猝死的易感性。这种疾病唯一确定的治疗方法是通过植入除颤器来预防猝死。在此,我们描述了一例患者,该患者表现为无休止的室性心动过速(VT)和晕厥,心电图表现为 1 型 Brugada 图形。该患者成功地用奎尼丁治疗后,出现了经典描述的 2 型和 3 型图形。

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引用本文的文献

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本文引用的文献

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Successful radiofrequency catheter ablation for electrical storm of ventricular fibrillation in a patient with Brugada syndrome.布加综合征患者室颤电风暴的成功射频导管消融治疗
Circ J. 2008 Jun;72(6):1025-9. doi: 10.1253/circj.72.1025.
2
Antiarrhythmic induced electrical storm in Brugada syndrome: a case report.抗心律失常药物诱发的 Brugada 综合征电风暴:一例报告
Ann Noninvasive Electrocardiol. 2007 Jul;12(3):274-8. doi: 10.1111/j.1542-474X.2007.00171.x.
3
Electrical storms in Brugada syndrome successfully treated with isoproterenol infusion and quinidine orally.Brugada 综合征伴电风暴患者经异丙肾上腺素静脉滴注和奎尼丁口服治疗成功。
Neth Heart J. 2007;15(4):151-5. doi: 10.1007/BF03085972.
4
Acute and chronic management in patients with Brugada syndrome associated with electrical storm of ventricular fibrillation.伴有心室颤动电风暴的Brugada综合征患者的急性和慢性管理
Heart Rhythm. 2007 Jun;4(6):695-700. doi: 10.1016/j.hrthm.2007.02.014. Epub 2007 Feb 20.
5
Brugada syndrome: report of the second consensus conference: endorsed by the Heart Rhythm Society and the European Heart Rhythm Association.布加综合征:第二届共识会议报告:得到心律学会和欧洲心律协会认可。
Circulation. 2005 Feb 8;111(5):659-70. doi: 10.1161/01.CIR.0000152479.54298.51. Epub 2005 Jan 17.
6
Electrical storm in Brugada syndrome successfully treated using isoprenaline.使用异丙肾上腺素成功治疗Brugada综合征电风暴。
Europace. 2004 Mar;6(2):130-3. doi: 10.1016/j.eupc.2003.11.009.
7
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Europace. 2003 Jul;5(3):257-61. doi: 10.1016/s1099-5129(03)00034-5.
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9
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