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肠壁囊样积气和气腹并发混合性结缔组织病

Pneumatosis intestinalis and pneumoperitoneum complicating mixed connective tissue disease.

作者信息

Pun Y L, Russell D M, Taggart G J, Barraclough D R

机构信息

Rheumatology, Unit, Royal Melbourne Hospital, Parkville, Victoria, Australia.

出版信息

Br J Rheumatol. 1991 Apr;30(2):146-9. doi: 10.1093/rheumatology/30.2.146.

DOI:10.1093/rheumatology/30.2.146
PMID:2012947
Abstract

A case of a young woman with a 3-year history of mixed connective tissue disease who developed secondary pneumatosis intestinalis and pneumoperitoneum and died shortly after of rapidly progressive disease is reported. The pathogenesis, treatment and prognosis of this unusual complication in mixed connective tissue disease are discussed.

摘要

报告了一例患有混合性结缔组织病3年的年轻女性病例,该患者出现了继发性小肠积气和腹腔积气,并在疾病快速进展后不久死亡。文中讨论了混合性结缔组织病中这种罕见并发症的发病机制、治疗方法及预后。

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Pneumatosis intestinalis and pneumoperitoneum complicating mixed connective tissue disease.肠壁囊样积气和气腹并发混合性结缔组织病
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Case Rep Med. 2012;2012:987410. doi: 10.1155/2012/987410. Epub 2012 Sep 29.
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