Department of Anesthesiology, University of Tokyo Hospital, 7-3-1 Hongo, Bunkyo-ku, Tokyo, Japan.
J Anesth. 2010 Apr;24(2):256-9. doi: 10.1007/s00540-010-0875-8. Epub 2010 Feb 6.
Parkes Weber syndrome is a rare disease characterized by overgrowth of an extremity linked to the presence of an arteriovenous malformation with multiple arteriovenous fistulas (AVFs). We report a patient with Parkes Weber syndrome with high-output cardiac failure due to multiple AVFs complicated by severe aortic regurgitation (AR) who required surgical treatment for AVFs. Division of the left deep femoral artery and banding of the left superficial femoral artery were performed. Such procedures can cause aggravation of AR and left ventricular failure due to the sudden increase in cardiac afterload. Pulmonary artery pressure, mixed venous oxygen saturation and cardiac index monitored by a thermodilution catheter, and a transesophageal echocardiography were useful in evaluating the effect of the surgical procedure and resultant acute increase in cardiac afterload on cardiac output and left ventricular function.
Parkes Weber 综合征是一种罕见的疾病,其特征是肢体过度生长,与存在多发性动静脉瘘(AVF)的动静脉畸形相关。我们报告了一例 Parkes Weber 综合征患者,因多发性 AVF 合并严重主动脉瓣反流(AR)导致心输出量过高性心力衰竭,需要手术治疗 AVF。行左股深动脉离断术和左股浅动脉结扎术。由于心脏后负荷的突然增加,此类手术可能导致 AR 和左心室衰竭加重。热稀释导管监测肺动脉压、混合静脉血氧饱和度和心指数,经食管超声心动图有助于评估手术过程及由此导致的心脏后负荷急性增加对心输出量和左心室功能的影响。