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法洛四联症修复术后主动脉根部瘤的内侧坏死

Medial necrosis in aortic root aneurysm after repair of tetralogy of Fallot.

作者信息

Crestanello Juan A, Cook Stephen, Daniels Curt, Hitchcock Charles L, Sai-Sudhakar Chittoor

机构信息

Division of Cardiothoracic Surgery, The Richard M. Ross Heart Hospital, The Ohio State University Medical Center, Columbus, Ohio 43210, USA.

出版信息

J Card Surg. 2010 Mar;25(2):230-2. doi: 10.1111/j.1540-8191.2009.00977.x. Epub 2010 Feb 9.

DOI:10.1111/j.1540-8191.2009.00977.x
PMID:20149016
Abstract

Aneurysmal dilatation of the aortic root occurs in some patients with tetralogy of Fallot (TOF) late after repair. It can lead to aortic valve insufficiency and rarely to aortic rupture or dissection. Aortic valve or aortic surgery is rarely performed in this group of patients. We present a case of aneurysmal dilatation of the ascending aorta treated with aortic valve sparing root replacement 43 years after the TOF repair. Histological examination of the aortic wall revealed medial necrosis. The implications of those finding and the timing of surgery are discussed.

摘要

法洛四联症(TOF)修复术后晚期,部分患者会出现主动脉根部瘤样扩张。这可能导致主动脉瓣关闭不全,极少情况下会导致主动脉破裂或夹层形成。该类患者很少进行主动脉瓣或主动脉手术。我们报告1例TOF修复术后43年升主动脉瘤样扩张患者,接受了保留主动脉瓣的根部置换术。主动脉壁组织学检查显示中层坏死。本文讨论了这些发现的意义及手术时机。

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1
Medial necrosis in aortic root aneurysm after repair of tetralogy of Fallot.法洛四联症修复术后主动脉根部瘤的内侧坏死
J Card Surg. 2010 Mar;25(2):230-2. doi: 10.1111/j.1540-8191.2009.00977.x. Epub 2010 Feb 9.
2
Aortic aneurysm formation five decades after tetralogy of Fallot repair.法洛四联症修复术后五十年出现主动脉瘤形成。
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引用本文的文献

1
Tetralogy of Fallot and aortic root dilation: a long-term outlook.法洛四联症与主动脉根部扩张:长期展望
Pediatr Cardiol. 2013 Apr;34(4):809-16. doi: 10.1007/s00246-012-0537-8. Epub 2012 Oct 19.