[颞下窝磷尿性间叶肿瘤所致的致癌性骨软化症]

[Oncogenic osteomalacia due to phosphaturic mesenchymal tumour in infratemporal fossa].

作者信息

Viscasillas Guillem, Maiz Javier, Lao Xavier, Zschaeck Christiane, Sanz Juan José

机构信息

Servicio ORL, Hospital Universitari Mútua de Terrassa, Barcelona, España.

出版信息

Acta Otorrinolaringol Esp. 2010 Sep-Oct;61(5):392-4. doi: 10.1016/j.otorri.2009.10.007. Epub 2010 Feb 20.

DOI:10.1016/j.otorri.2009.10.007

PMID:20172500

Abstract

Oncogenic osteomalacia is an uncommon syndrome characterized by phosphaturic tumours that produce mineral metabolism abnormalities. Head and neck is the second most frequent location of these tumours. We describe a case of a phosphaturic mesenchymal tumour in the infratemporal fossa that caused oncogenic osteomalacia, resolved by means of surgical excision.

摘要

肿瘤性骨软化症是一种罕见综合征，其特征为产生矿物质代谢异常的磷尿性肿瘤。头颈部是这些肿瘤第二常见的发病部位。我们描述了一例发生于颞下窝的磷尿性间叶肿瘤导致肿瘤性骨软化症的病例，该病例通过手术切除得以治愈。