Ahmed Mohamed Khalifa, Ishino Takashi, Hirakawa Katsuhiro, Arihiro Koji
Department of Otorhinolaryngology, Head & Neck Surgery, Graduate School of Biomedical Sciences, Hiroshima University, 1-2-3 Kasumi, Minami-ku, Hiroshima city, Hiroshima, 734-8551 Japan.
Auris Nasus Larynx. 2010 Aug;37(4):519-21. doi: 10.1016/j.anl.2009.11.002. Epub 2010 Feb 20.
First described in 1969, syringoid eccrine carcinoma (SEC) is a rare cutaneous tumor with some controversy regarding its correct definition. It consists of solid nests and small cords in a dense fibrocollagenous stroma. As it is rare, its clinical appearance is not well characterized and its biological behaviour is not defined. It usually affects skin of the scalp, extremities and more rarely, other sites. It behaves as locally aggressive tumor but metastases are rare. Although there have been some previous reports describing clinical presentation and management of SEC in the skin, there has been no previous reports describing clinical findings and management of this tumor in the external auditory canal. We report a case of a 57-year-old female with small solitary mass in left external auditory canal associated with discharge, severe itching and bleeding on manipulation. Complete local excision is the recommended method for diagnosis and treatment of this tumor in the external auditory canal. This extremely rare case serves as a springboard for the diagnosis as well as the management of SEC in external auditory canal.
1969年首次被描述，管状小汗腺癌（SEC）是一种罕见的皮肤肿瘤，关于其正确定义存在一些争议。它由致密纤维胶原基质中的实性巢状结构和小条索组成。由于其罕见，其临床表现特征不明显，生物学行为也不明确。它通常累及头皮、四肢皮肤，较少累及其他部位。它表现为局部侵袭性肿瘤，但转移罕见。尽管之前有一些报告描述了皮肤SEC的临床表现和治疗，但之前没有关于外耳道这种肿瘤的临床发现和治疗的报告。我们报告一例57岁女性，左外耳道有一个小的孤立肿块，伴有分泌物、严重瘙痒和触诊时出血。对于外耳道这种肿瘤，推荐采用完整局部切除进行诊断和治疗。这个极其罕见的病例为外耳道SEC的诊断和治疗提供了一个切入点。
