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一名患有先天性袋状结肠的尼泊尔儿童罕见先天性畸形的报告:病例报告。

A report of a rare congenital malformation in a Nepalese child with congenital pouch colon: a case report.

作者信息

Shakya Vikal Chandra, Agrawal Chandra Shekhar, Koirala Rabin, Khaniya Sudeep, Poudel Prakash, Adhikary Shailesh

机构信息

Department of Surgery, B P Koirala Institute of Health Sciences, Dharan, P.O. Box 7053, Kathmandu, Nepal.

出版信息

Cases J. 2009 Mar 10;2:6424. doi: 10.1186/1757-1626-0002-0000006424.

DOI:10.1186/1757-1626-0002-0000006424
PMID:20181156
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2827101/
Abstract

Congenital pouch colon is one of rare congenital anomalies. We report a 3-day-old male child with congenital pouch colon who underwent a window colostomy but died because of overwhelming sepsis. Due to its rarity, many surgeons in our part of the world may not be aware of it, hence increasing the potential to its mismanagement. However, with simple keen observations, we can safely come to its diagnosis. The aim of this report is to bring attention to congenital pouch colon associated with anorectal malformation in our country, with a brief emphasis on an approach to its diagnosis and initial management.

摘要

先天性袋状结肠是一种罕见的先天性畸形。我们报告一例3日龄患有先天性袋状结肠的男婴,该患儿接受了开窗结肠造口术,但因严重脓毒症死亡。由于其罕见性,在我们所在地区的许多外科医生可能并不知晓,从而增加了处理不当的可能性。然而,通过简单敏锐的观察,我们能够安全地做出诊断。本报告的目的是引起我国对与肛门直肠畸形相关的先天性袋状结肠的关注,并简要强调其诊断方法和初始处理。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b58/2827101/ae3091319a51/1757-1626-0002-0000006424-5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b58/2827101/1d8dd65a84eb/1757-1626-0002-0000006424-1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b58/2827101/98edea8b9382/1757-1626-0002-0000006424-2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b58/2827101/363b82efca99/1757-1626-0002-0000006424-3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b58/2827101/7e9d33c1188b/1757-1626-0002-0000006424-4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b58/2827101/ae3091319a51/1757-1626-0002-0000006424-5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b58/2827101/1d8dd65a84eb/1757-1626-0002-0000006424-1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b58/2827101/98edea8b9382/1757-1626-0002-0000006424-2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b58/2827101/363b82efca99/1757-1626-0002-0000006424-3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b58/2827101/7e9d33c1188b/1757-1626-0002-0000006424-4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/0b58/2827101/ae3091319a51/1757-1626-0002-0000006424-5.jpg

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