Bendayan P, Glock Y, Dislaire I, Duboucher C, Bugat R, Tredez J, Conte D
Service de Chirurgie Cardio-vasculaire, CHU de Rangueil, Toulouse.
Ann Chir. 1991;45(2):149-54.
The authors report a case of leiomyosarcoma (LMS) of the second segment of the inferior vena (IVC) with liver metastasis. Treatment by surgery and chemotherapy proved to be effective, as the patient is asymptomatic 8 years after the first operation. A review of the literature shows that these tumours are rare and have a slow course. The symptoms are often relatively minor and depend on the caval segment involved. The best examination for positive and topographic diagnosis remains computed tomography, but MR Imaging is promising. The prognosis remains severe (mean survival: 2 years) and surgery is the main treatment, with various techniques according to the caval segment involved.
作者报告了一例下腔静脉(IVC)第二段平滑肌肉瘤(LMS)伴肝转移的病例。手术和化疗治疗被证明是有效的,因为患者在首次手术后8年无症状。文献回顾显示,这些肿瘤罕见且病程缓慢。症状通常相对较轻,取决于受累的腔静脉段。计算机断层扫描仍然是阳性和定位诊断的最佳检查方法,但磁共振成像也很有前景。预后仍然严峻(平均生存期:2年),手术是主要治疗方法,根据受累的腔静脉段采用不同的技术。