Fischbach R, Deutsch H J, Neufang K F, Féaux de Lacroix W
Institut und Poliklinik für Radiologische Diagnostik, Universität zu Köln.
Aktuelle Radiol. 1991 Jan;1(1):43-5.
The case of a woman of 48 years of age suffering from pulmonary lymphangiomyomatosis is presented. Chest radiographs showed the reticular infiltrate of diffuse interstitial lung disease, whereas high resolution CT illustrated multiple, well-defined cystic lesions distributed diffusely through the lungs without fibrotic changes or nodular densities. The patient underwent open lung biopsy and pleurodesis because of recurrent pneumothorax. Treatment with medroxyprogesterone was initiated.
本文介绍了一名48岁患有肺淋巴管平滑肌瘤病的女性病例。胸部X光片显示弥漫性间质性肺病的网状浸润，而高分辨率CT显示肺部弥漫分布着多个边界清晰的囊性病变，无纤维化改变或结节状密度。由于复发性气胸，患者接受了开胸肺活检和胸膜固定术。开始使用甲羟孕酮进行治疗。
