Kumazaki S, Mishima H, Nishimiya K, Ishihara T, Yamada R, Uzawa T, Suematsu N
Nihon Kyobu Shikkan Gakkai Zasshi. 1989 Jul;27(7):860-5.
A 35-year-old unmarried woman was admitted to our hospital because of right pneumothorax. Pulmonary lymphangiomyomatosis was suspected from CT and transbronchial lung biopsy findings. The diagnosis was confirmed histologically by open lung biopsy. As her biopsy specimen showed positive findings for both estrogen and progesterone receptor, tamoxifen administration was started. The CT revealed multiple cystic lesions (5-10 mm in diameter) but otherwise normal vascular structures and normal lung density. The plain chest radiograph showed no abnormalities. CT is very useful for the early detection of pulmonary lymphangiomyomatosis.
一名35岁未婚女性因右侧气胸入住我院。根据CT及经支气管肺活检结果怀疑为肺淋巴管平滑肌瘤病。通过开胸肺活检在组织学上确诊。由于她的活检标本雌激素和孕激素受体均呈阳性，遂开始给予他莫昔芬治疗。CT显示多个囊性病变（直径5 - 10毫米），但血管结构及肺密度正常。胸部X线平片未见异常。CT对肺淋巴管平滑肌瘤病的早期检测非常有用。
