St. Vincent's Catholic Medical Center, 170 W 12th St., New York, NY 10011, USA.
Clin Imaging. 2010 Mar-Apr;34(2):138-42. doi: 10.1016/j.clinimag.2009.09.003.
Susac syndrome is a rare neurologic disorder first described by Susac et al. in 1979. Clinically, Susac syndrome consists of a triad including encephalopathy, branch retinal artery occlusion, and sensorineural hearing loss. Microinfarction is believed to be the basic histologic feature and MR is considered the best imaging modality. This case documents the typical imaging findings of Susac syndrome, as well as the unique MR imaging finding of cranial nerve enhancement.
苏萨克综合征是一种罕见的神经系统疾病,由 Susac 等人于 1979 年首次描述。临床上,苏萨克综合征由三联征组成,包括脑病、视网膜动脉分支阻塞和感觉神经性听力损失。微梗死被认为是基本的组织学特征,磁共振成像(MRI)被认为是最佳的成像方式。本病例记录了苏萨克综合征的典型影像学表现,以及颅神经增强的独特 MRI 影像学发现。